Parry Romberg Syndrome with contralateral iridocorneal endothelial syndrome: a unique case

Authors

  • Usha K. Raina Department of Ophthalmology, Guru Nanak Eye Centre, Maulana Azad Medical College, Delhi, India
  • Shruti Bhattacharya Department of Ophthalmology, Guru Nanak Eye Centre, Maulana Azad Medical College, Delhi, India
  • Prateeksha Sharma Department of Ophthalmology, Guru Nanak Eye Centre, Maulana Azad Medical College, Delhi, India
  • Varun Saini Department of Ophthalmology, Guru Nanak Eye Centre, Maulana Azad Medical College, Delhi, India

DOI:

https://doi.org/10.18203/2349-3933.ijam20214527

Keywords:

Parry Romberg syndrome, ICE syndrome, Hemifacial atrophy, Glaucoma

Abstract

Parry-Romberg syndrome (PRS) is a rare disorder which causes progressive hemifacial atrophy, with ocular manifestations like hypotony, enophthalmos and corneal edema on the ipsilateral atrophic side. This is a report of a unique case of PRS with contalateral manifestations like ectropion uvea, correctopia and endothelial deposits, along with polymegathism and pleomorphism seen on specular microscopy suggestive of Iridocorneal Endothelial (ICE) Syndrome. ICE syndrome and PRS have not been reported together in any literature so far. This case highlights the importance of a thorough glaucoma workup and corneal examination on the atrophic facial side as well as on the apparently normal side in all cases of PRS.

References

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Published

2021-11-23

Issue

Section

Case Reports